PROGRESSION OF PULMONARY ALVEOLAR MICROLITHIASIS TO PULMONARY HYPERTENSION AND COR PULMONALE
نویسندگان
چکیده
منابع مشابه
A Case Report of Pulmonary Alveolar Microlithiasis
Pulmonary alveolar microlithiasis is a rare autosomal recessive disease characterized by the formation of calcium phosphate deposition in the alveoli. Although the disease most often occurs in children, most patients with the disease are diagnosed in adulthood due to the slow progression of the disease inside the lungs. In childhood, it often causes no symptoms, and changes in the lung parenchy...
متن کاملPulmonary Alveolar Microlithiasis: A Rare Case Report
Pulmonary alveolar microlithiasis is an uncommon infiltrative pulmonary disease characterized by deposition of microliths in the alveoli. We present the case of a young adult with complaints of shortness of breath on exertion. Chest radiograph showed innumerable small, dense nodules, diffusely involving both the lungs - predominantly in the lower zones. High-resolution CT scan illustrated wides...
متن کاملPulmonary hypertension and chronic cor pulmonale in COPD
Hypoxia and endothelial dysfunction play a central role in the development of pulmonary hypertension. Cor pulmonale is a maladaptive response to pulmonary hypertension. The presence of peripheral edema in cor pulmonale is almost invariably associated with hypercapnia. Correction of abnormalities of gas exchange and ventilation can ameliorate pulmonary hypertension and improve survival. This rev...
متن کامل[Pulmonary alveolar microlithiasis].
The authors present two of their own observations where, based on the clinical course of the disease and the X-ray finding, they diagnosed the condition as pulmonary alveolar microlithiasis. They present a review of the literature as regards new views on the pathogenesis, diagnosis and therapy of the condition. They evaluate the contribution of scintigraphy 99 mTc, bronchial lavage and X-ray me...
متن کاملPulmonary alveolar microlithiasis.
Case report from a 12-years old russian girl with pulmonary alveolar microlithiasis. The diagnosis was confirmed by histologic examination from biopsy specimen of the lung. The differential diagnosis and the histomorphology are discussed.
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ژورنال
عنوان ژورنال: Chest
سال: 2019
ISSN: 0012-3692
DOI: 10.1016/j.chest.2019.08.1597